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PubMed · 9835964

[Multiple trichodiscomas associated with colonic polyposis].

T Le Guyadec·J P Dufau·J F Poulain·F Vaylet·M Grossin·G Lanternier
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Abstract

BACKGROUND: Trichodiscoma is an uncommon benign tumor of the pilosebaceous system. CASE REPORT: An 83-year-old man had a past history of adenomatous polyps of the colon. The subject's brother had died from cancer of the colon. Over the past 4 years, the patient had developed approximately 30 small asymptomatic papulonodular tumors on the trunk. Skin biopsy demonstrated trichodiscomas. DISCUSSION: Together with fibrofolliculomas and perifollicular fibromas, trichodiscomas are benign tumors of the pilosebaceous system. These different tumors may occur simultaneously as in Birt-Hogg-Dubé syndrome which associates trichodiscoma and familial colonic polyposis. This combination has only been reported in Birt-Hogg-Dubé syndrome or with perifollicular fibromas. CONCLUSION: This case suggests that patients with hamartomas of the pilosebaceous system should undergo explorations in search for digestive tract polyposis.

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Adenomatous Polyposis ColiAgedAged, 80 and overBiopsyHamartomaHumansMaleNeoplasms, Multiple PrimarySkinSkin NeoplasmsSyndromeCase ReportsEnglish AbstractJournal Article

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T Le Guyadec, J P Dufau, J F Poulain, F Vaylet, M Grossin, G Lanternier. 1998. [Multiple trichodiscomas associated with colonic polyposis].. https://pubmed.ncbi.nlm.nih.gov/9835964/

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