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PubMed · 657840

Pseudoxanthoma elasticum.

M W Engelman·M T Fliegelman
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Abstract

Pseudoxanthoma elasticum (PXE) is a genetic disorder of connective tissue with multi-systemic manifestations. Although the skin changes are striking, the eye and cardiovascular lesions can be most devastating to the patient. A review of the clinical and pathologic findings and recent therapeutic approaches is presented. Recent investigations on the pathogenesis and genetics of PXE are also discussed.

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Cardiovascular DiseasesEyeHumansPseudoxanthoma ElasticumSkinJournal Article

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M W Engelman, M T Fliegelman. 1978. Pseudoxanthoma elasticum.. https://pubmed.ncbi.nlm.nih.gov/657840/

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