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PubMed · 7295065

[Metachromatic leukodystrophy (pathogenesis and pathological anatomy)].

M K Nedz'ved'·S K Kletskiĭ
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Abstract

An observation of metachromatic leukodystrophy in a child is described indicating the main criteria for macroscopic and histological diagnosis. The authors believe demyelinization and loss of oligodendroglia in this disease to be due to the toxic effect of excess sulphatides and derivatives thereof.

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AutopsyBrainFemaleGallbladderHumansInfantKidneyLeukodystrophy, MetachromaticCase ReportsEnglish AbstractJournal Article

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M K Nedz'ved', S K Kletskiĭ. 1981. [Metachromatic leukodystrophy (pathogenesis and pathological anatomy)].. https://pubmed.ncbi.nlm.nih.gov/7295065/

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