Neurofibromatosis.

K L Roos; M Muckway

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PubMed · 7712636

Neurofibromatosis.

K L Roos·M Muckway

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Abstract

The neurofibromatoses are defined by the presence of café-au-lait macules and neurofibromas and are associated with central and peripheral nervous system tumors. Individuals with neurofibromatosis 1 are at risk for optic nerve gliomas, nerve root and plexi neurofibromas and schwannomas, spinal cord tumors, benign and malignant peripheral nerve sheath tumors, and pheochromocytomas. Individuals with neurofibromatosis 2 are at risk for presenile cataracts, vestibular schwannomas, intracranial and intraspinal meningiomas, and intramedullary spinal cord ependymomas.

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Child Child, Preschool Cranial Nerve Neoplasms Humans Infant Neurofibroma, Plexiform Neurofibromatosis 1 Neurofibromatosis 2 Optic Nerve Diseases Pigmentation Disorders Skin Neoplasms Soft Tissue Neoplasms Spinal Cord Neoplasms Vestibular Nerve Journal Article Review

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K L Roos, M Muckway. 1995. Neurofibromatosis.. https://pubmed.ncbi.nlm.nih.gov/7712636/

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